Chronic intestinal pseudo-obstruction (CIP) is the name given to a number of rare disorders that cause impaired gastrointestinal motility (movement in the digestive tract). A diagnosis of CIP is based on symptoms that occur when the intestine is blocked and on clinical findings. In pseudo-obstruction, the symptoms are caused not by a surgically correctable tumor, twist, or ulcer in the bowel, but by a problem having to do with the strength or coordination of the contractions that move along the contents of the bowel.
Fact Sheet: Antroduodenal Manometry: Questions and Answers811
Your child is scheduled for a specialized test called antroduodenal manometry. This information will help to prepare you and your child so the experience is as successful as it can be.
Fact Sheet: Colon Manometry: Questions and Answers812
Your child is scheduled for a specialized test called colon manometry that will check the motility of the colon. This guide will help to prepare you and your child so that the experience is as successful as it can be.Topics: Anal, Rectal Disorders, Colonic inertia, Pseudo-obstruction, Hirschsprung's Disease, Motility, Tests, lower GI tract
Fact Sheet: Cyclic Vomiting Syndrome817
Cyclic vomiting syndrome (CVS) was first described about 120 years ago by Dr. Samuel Gee, the erudite British physician. Interest in the syndrome was revived when Kathleen Adams, a parent of an affected child founded the Cyclic Vomiting Syndrome Association in 1993. She enlisted the support of pediatric gastroenterologists, Drs. David Fleisher and B.U.K. Li, who recognized that better treatment of the disorder would only occur if the syndrome could be scientifically defined for medical researchers. This article describes CVS and approaches to treatment.Topics: CVS, Motility, Nausea, vomiting, Nausea, vomiting, Other Disorders/Symptoms, Other Disorders/Symptoms, Stomach Disorders, Stomach Disorders
Over 1,000 new cases of Hirschsprung's disease are diagnosed in the USA every year. More than half the children treated appropriately with surgery for Hirschsprung's disease suffer from chronic problems with constipation, incontinence, and/or abdominal pain. Even as adults, over half will experience occasional episodes of incontinence, and 10% will endure constipation unresponsive to medical management. Nonetheless, adjustment for teenagers and young adults with Hirschsprung's disease is not different than for healthy children; successful adjustment depends largely on family support. Revised and updated 2009.Topics: Anal, Rectal Disorders, Constipation, difficult to pass stools, Constipation, difficult to pass stools, Fecal soiling, incontinence, Hirschsprung's Disease, Incontinence, Motility
Fact Sheet: Hirschsprung’s Disease in Children and Adults839
Hirschsprung’s disease is an illness that people are born with (congenital), in which there is a lack of nerve cells (ganglion cells) in the segments of the intestinal tract located in the colon or rectum. Since the first operative curative technique for Hirschsprung’s disease was described in 1948, progress in diagnostic methods and surgical techniques have allowed the survival and successful treatment of most children with Hirschsprung’s disease. In spite of these advances, postoperative problems continue to occur. Recently, research has produced a better understanding of the disease, knowledge that will undoubtedly lead to further refinements of the surgical techniques and better treatment of these patients.
Hirschsprung’s disease is a rare illness that people are born with (congenital). It occurs annually in about 1 in 5,000 live births. In Hirschsprung’s disease there is a lack of nerve cells (ganglion cells) in segments of the intestinal tract located in the colon and/or rectum.
The treatment is surgery to remove the abnormal bowel segment and restore bowel continuity. Following surgical treatment, most children have a good outcome, but some have persistent bowel problems such as constipation, soiling, fecal incontinence, and inflammation in the colon (enterocolitis). These symptoms can impact the quality of life, which also needs to be addressed.
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